Dr. Ankita Narula, Dr. Ruma Das, Dr. Tshering Wangchuk, Dr. Mohit Ganesh Bharambe
BACKGROUND : Pulsatile proptosis is a clinical symptom characterized by protrusion and pulsation of the eyeball that can occur due to various causes like carotico-cavernous fistulas, neurofibromatosis type 1, arteriovenous malformation, trauma, arachnoid cyst.
CASE REPORT : We present here the clinical and radiological features of a 35 yrs old female who presented to us with pulsatile proptosis of her right eye and vascular swelling with a bruit in her right upper lid along with generalised weakness of her body with possibility of cerebro-facial arteriovenous metameric syndrome.The clinical findings,differential diagnosis and the possible management in such a case is being discussed here.
CONCLUSION : Unilateral exophthalmos can be caused by both intraorbital and extraorbital vascular malformations.2 The differential diagnosis includes anterior cranial fossa dural fistulas, cirsoid aneurysms of the scalp, traumatic carotid-cavernous fistulas, and congenital vascular malformations like Wyburn-Mason or Bonnet-Dechaunne-Blanc syndrome.