Dr. Reena Gupta, G12626, Dr. Chekitaan Singh, Dr. Neebha Anand, Dr. Ashok Kumar Khurana
To report a rare case of congenital brown syndrome associated with hydrocephalus, dermoid, preauricular tag and ocular torticollis. We treated a 13 year old female who was a case of unilateral brown syndrome with head tilt and chin up with epibulbar dermoid in the fellow eye and preauricular tag on contralateral ear. Her BCVA was 6/6 in R/E , 6/18 in L/E. Orthoptic evaluation revealed esotropia of 60 BO with hypotropia of 15 PD in primary gaze and had marked limitation of upward movement in adduction. She had moderate amblyopia in affected eye due to delayed treatment. Her primary concern was cosmetic and we did a two stage procedure- silicon band expander was done for hypotropia and horizontal surgery for residual esotropia. After 6 months of follow up she is doing cosmetically well. This case has been presented to increase awareness about such rare associations having a common embryological origin suggesting a craniofacial syndrome variant not documented so far.