Dr. Divya Handa, Dr. Krishna Addoor Rao, Dr. Vijaya Paih, Dr. Akshay Sehgal, Dr. Namitha Rachel Mathew
PURPOSE : To report a rare case of unilateral orbital lymphovenous malformation with persistent fetal vasculature
METHODS : We report 9 year old male presenting with vision diminution and reddish mass in right eye
RESULTS : His best corrected visual acuity was counting finger 1 meter (right eye), 6/9 (left eye). Right eye had 15 degree esotropia, leucocoria, microphthalmia, reddish vascular conjunctival mass, posterior subcapsular cataract and persistent fetal vasculature. Left eye, systemic examination were normal.Contrast Enhanced CT orbit showed orbital lymphovenous malformation. Child’s parents were counseled and were given option of surgery but they opted for observation
CONCLUSION : Literature search revealed persistent fetal vasculature with lymphovenous malformation has not been reported. Persistent fetal vasculature is a rare defect with leucocoria, poor vision, squint and cataract. Lymphatic malformations are uncommon benign vascular tumors and less likely to cause visual compromise.