Dr. Pavitraa P, P18816, Dr. Vasumathi Kannabiran, Dr. Waheeda Nazir
Developmental anomaly causing bilobed lens with anterior segment dysgenesis is an extremely rare condition. Here we report a case of 12 years old boy who presented with defective vision in the left eye since childhood. His visual acuity was 6/6 in RE and 1/60 in LE.IOP was normal in both eyes. Examination of RE was normal. LE showed megalocornea with posterior embryotoxon in medial and lateral sides, abnormal pigmented tissue noted from 1to 3 o’ clock position behind the iris and lens, corectopic pupil and bilobed lens with minimal cataractous changes with zonular fibres in between the two lobes. Fundus- chorioatrophic patch in the superotemporal quadrant. Gonioscopy showed detached Schwalbe’s line with open angles and iris process in medial and temporal quadrants. Bilobed lens with single posterior capsule was confirmed by B scan and UBM.UBM also showed abnormal fibres between the two lobes of lens and poor development of ciliary body and zonules in medial and temporal quadrants.