Dr. Meenakshi Wadhwani, W10817, Dr. Amar Ranjan
Background : Esthesioneuroblastoma (ENB) is a rare neuroepithelial tumor arising from the olfactory epithelium in the cribriform plate or nasal cavity. It accounts for 1 to 5% cases of malignant neoplasms of nasal cavity.
Methods : The Clinical records, radiological and histopathological findings and treatment findings of a patient with esthesioneuroblastoma are reported.
Discussion : A 20 year old pregnant female presenting as painful loss of vision in both eyes, on imaging diagnosed as meningioma. However, histopathology of fluid obtained after craniotomy showed esthesioneuroblastoma. She underwent extensive radiotherapy but died within three months of diagnosis.
Conclusion : This case highlights the progressive and fatal course of olfactory neuroblastoma as they can present with the complex symptoms related to ocular and nasal sites,timely referral of patients presenting with visual symptoms along with nasal involvement (frequent epistaxis) to otorhinolaryingologists is very important.